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SARDH rabbit pAb
商品货号: PLA021021
WB IHC ELISA
¥600元
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MSDS
说明书
商品描述
  • 基因名称: SARDH DMGDHL1
  • 蛋白名称: SARDH
  • Human_gene_id: 1757
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=1757
  • Human_swiss_prot_no: Q9UL12
  • Human_swiss_link: https://www.uniprot.org/uniprotkb/Q9UL12/entry
  • Mouse_gene_id: 192166
  • Mouse_gene_link: https://www.uniprot.org/uniprot/192166
  • Mouse_swiss_prot_no: Q99LB7
  • Mouse_swiss_link: https://www.uniprot.org/uniprotkb/Q99LB7
  • Rat_gene_id: 114123
  • Rat_gene_link: https://www.uniprot.org/uniprot/114123
  • Rat_swiss_prot_no: Q64380
  • Rat_swiss_link: https://www.uniprot.org/uniprotkb/Q64380
  • 特异性: This antibody detects endogenous levels of SARDH at Human/Mouse/Rat
  • 组成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 来源: Polyclonal, Rabbit,IgG
  • 稀释: WB 1:500-2000;IHC-p 1:50-300; ELISA 2000-20000
  • 纯化工艺: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • 浓度: 1 mg/ml
  • 储存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 说明书: 1
  • Msds: MSDS_Antibody.pdf
  • 分子量: 101kD
  • 功能: catalytic activity:Sarcosine + acceptor + H(2)O = glycine + formaldehyde + reduced acceptor.,cofactor:Binds 1 FAD covalently per monomer.,disease:Defects in SARDH are a ause of sarcosinemia [MIM:268900]. Sarcosinemia is a metabolic disorder characterized by an increased concentration of sarcosine in plasma and urine due to sarcosine dehydrogenase deficiency. Prevalence has been estimated at 1:28'000 to 1:350'000 in newborn screening programs. Sarcosinemia is most probably a benign condition without significant clinical problems. It is transmitted in an autosomal recessive manner.,pathway:Amine and polyamine degradation; sarcosine degradation; formaldehyde and glycine from sarcosine: step 1/1.,similarity:Belongs to the gcvT family.,
  • 相关产品: RS0001,RS0002,YM3028,YM3029
  • 细胞定位: Mitochondrion matrix .
  • 组织表达: Expressed in pancreas, liver and kidney.
  • 科研货号: PLA021021
SARDH rabbit pAb
Catalog No PLA021021
Product information
  • 基因名称: SARDH DMGDHL1
  • 蛋白名称: SARDH
  • Human_gene_id: 1757
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=1757
  • Human_swiss_prot_no: Q9UL12
  • Human_swiss_link: https://www.uniprot.org/uniprotkb/Q9UL12/entry
  • Mouse_gene_id: 192166
  • Mouse_gene_link: https://www.uniprot.org/uniprot/192166
  • Mouse_swiss_prot_no: Q99LB7
  • Mouse_swiss_link: https://www.uniprot.org/uniprotkb/Q99LB7
  • Rat_gene_id: 114123
  • Rat_gene_link: https://www.uniprot.org/uniprot/114123
  • Rat_swiss_prot_no: Q64380
  • Rat_swiss_link: https://www.uniprot.org/uniprotkb/Q64380
  • 特异性: This antibody detects endogenous levels of SARDH at Human/Mouse/Rat
  • 组成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 来源: Polyclonal, Rabbit,IgG
  • 稀释: WB 1:500-2000;IHC-p 1:50-300; ELISA 2000-20000
  • 纯化工艺: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • 浓度: 1 mg/ml
  • 储存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 说明书: 1
  • Msds: MSDS_Antibody.pdf
  • 分子量: 101kD
  • 功能: catalytic activity:Sarcosine + acceptor + H(2)O = glycine + formaldehyde + reduced acceptor.,cofactor:Binds 1 FAD covalently per monomer.,disease:Defects in SARDH are a ause of sarcosinemia [MIM:268900]. Sarcosinemia is a metabolic disorder characterized by an increased concentration of sarcosine in plasma and urine due to sarcosine dehydrogenase deficiency. Prevalence has been estimated at 1:28'000 to 1:350'000 in newborn screening programs. Sarcosinemia is most probably a benign condition without significant clinical problems. It is transmitted in an autosomal recessive manner.,pathway:Amine and polyamine degradation; sarcosine degradation; formaldehyde and glycine from sarcosine: step 1/1.,similarity:Belongs to the gcvT family.,
  • 相关产品: RS0001,RS0002,YM3028,YM3029
  • 细胞定位: Mitochondrion matrix .
  • 组织表达: Expressed in pancreas, liver and kidney.
  • 科研货号: PLA021021
  • Hunan UPT Biotechnology Co.,Ltd
    Website:www.uptbio.com Servive hotline :4006916686
    E-mail:service@uptbio.com
    Address:
    Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.
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